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An Entity of Type: disease, from Named Graph: http://dbpedia.org, within Data Space: dbpedia.org

T cell deficiency disease that is the result of a large deletion of chromosome 22, which includes the DGS gene needed for development of the thymus and related glands with subsequent lack of T-cell production

Property Value
dbo:complications
  • Kidney problems,hearing loss,autoimmune disorders
dbo:description
  • ରୋଗ (or)
  • Krankheit (de)
  • malattia umana (it)
  • хвороба (uk)
  • תסמונת גנטית (iw)
  • oireyhtymä (fi)
  • bolest nedostatka T ćelija koja je rezultat velikog brisanja hromosoma 22, koji uključuje DGS gen potreban za razvoj timusa i srodnih žlijezda s naknadnim nedostatkom proizvodnje T ćelija (bs)
  • T cell deficiency disease that is the result of a large deletion of chromosome 22, which includes the DGS gene needed for development of the thymus and related glands with subsequent lack of T-cell production (en)
  • veleszületett betegség (hu)
  • Pathologie en rapport avec une microdélétion d'une région chromosomale (fr)
dbo:differentialDiagnosis
dbo:diseasesDB
  • 3631
dbo:eMedicineSubject
  • med (en)
dbo:eMedicineTopic
  • 567 (en)
dbo:geneReviewsId
  • NBK1523
dbo:geneReviewsName
  • 22q11.2 Deletion Syndrome (en)
dbo:gradName
  • 22q112-deletion-syndrome
dbo:gradNum
  • 10299
dbo:icd10
  • D82.1
dbo:icd9
  • ,
  • 279.11
  • 758.32
dbo:medicalCause
dbo:medicalDiagnosis
dbo:meshId
  • D004062
dbo:nord
  • chromosome-22q11-2-deletion-syndrome
dbo:omim
  • 188400 (xsd:integer)
dbo:orpha
  • 567
dbo:symptom
dbo:thumbnail
dbo:treatment
dbo:wikiPageExternalLink
dbo:wikiPageWikiLink
dbp:caption
  • Enzo, a man with chromosome 22 deletion syndrome . (en)
dbp:causes
dbp:complications
  • Kidney problems, hearing loss, autoimmune disorders (en)
dbp:curlie
  • Health/Conditions_and_Diseases/Genetic_Disorders/DiGeorge_Syndrome/ (en)
dbp:diagnosis
  • Based on symptoms and genetic testing (en)
dbp:differential
dbp:diseasesdb
  • 3631 (xsd:integer)
dbp:emedicinesubj
  • med (en)
dbp:emedicinetopic
  • 567 (xsd:integer)
dbp:field
dbp:frequency
  • 1 (xsd:integer)
dbp:gardname
  • 22 (xsd:integer)
dbp:gardnum
  • 10299 (xsd:integer)
dbp:genereviewsname
  • 22 (xsd:integer)
dbp:genereviewsnbk
  • NBK1523 (en)
dbp:icd
  • 279.110000 (xsd:double)
  • 758.320000 (xsd:double)
  • (en)
  • , (en)
  • D82.1 (en)
dbp:meshid
  • D004062 (en)
dbp:name
  • DiGeorge syndrome (en)
dbp:nord
  • chromosome-22q11-2-deletion-syndrome (en)
dbp:omim
  • 188400 (xsd:integer)
dbp:orphanet
  • 567 (xsd:integer)
dbp:prognosis
  • Depends on the specific symptoms (en)
dbp:symptoms
  • Varied; commonly congenital heart problems, specific facial features, cleft palate (en)
dbp:synonyms
  • DiGeorge anomaly, velocardiofacial syndrome , Shprintzen syndrome, conotruncal anomaly face syndrome , Takao syndrome, Sedlackova syndrome, Cayler cardiofacial syndrome, CATCH22, 22q11.2 deletion syndrome (en)
dbp:treatment
dbp:wikiPageUsesTemplate
dbp:wordnet_type
dct:subject
rdf:type
rdfs:label
  • DiGeorge syndrome (en)
  • متلازمة دي جورج (ar)
  • DiGeorgův syndrom (cs)
  • Mikrodeletionssyndrom 22q11 (de)
  • Síndrome de DiGeorge (es)
  • Syndrome de délétion 22q11.2 (fr)
  • Sindrom delesi 22q11 (in)
  • Sindrome da delezione 22q11 (it)
  • 디조지 증후군 (ko)
  • 22q11.2欠失症候群 (ja)
  • Síndrome de DiGeorge (pt)
  • Zespół delecji 22q11.2 (pl)
  • Velocardiofaciaal syndroom (nl)
  • Синдром Ди Георга (ru)
  • Синдром Ді Георга (uk)
  • 22q11-deletionsyndromet (sv)
  • 迪喬治症候群 (zh)
owl:sameAs
prov:wasDerivedFrom
foaf:depiction
foaf:isPrimaryTopicOf
foaf:name
  • DiGeorge syndrome (en)
is dbo:differentialDiagnosis of
is dbo:knownFor of
is dbo:wikiPageRedirects of
is dbo:wikiPageWikiLink of
is dbp:content of
is dbp:differential of
is foaf:primaryTopic of
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